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Adenohypophysitis

MedGen UID:
1677203
Concept ID:
C5190880
Disease or Syndrome
Synonyms: adenohypophysis inflammation; adenohypophysitis; Anterior pituitary hypophysitis; anterior pituitary hypophysitis; inflammation of adenohypophysis; lymphocytic adenohypophysitis
SNOMED CT: Anterior pituitary hypophysitis (783243008); Adenohypophysitis (783243008)
 
Monarch Initiative: MONDO:0019838
Orphanet: ORPHA95512

Definition

A rare acquired pituitary hormone deficiency a type of primary hypophysitis with characteristics of inflammation of anterior pituitary. Clinical presentation is variable and includes headaches, visual disturbances, and symptoms of adrenal insufficiency, hyperprolactinaemia, hypothyroidism and hypogonadism. It most commonly affects young women during pregnancy or postpartum period. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdenohypophysitis

Professional guidelines

PubMed

Donegan D, Saeed Z, Delivanis DA, Murad MH, Honegger J, Amereller F, Oguz SH, Erickson D, Bancos I
J Clin Endocrinol Metab 2022 Mar 24;107(4):1170-1190. doi: 10.1210/clinem/dgab839. PMID: 35137155Free PMC Article
Chiloiro S, Tartaglione T, Angelini F, Bianchi A, Arena V, Giampietro A, Mormando M, Sciandra M, Laino ME, De Marinis L
Neuroendocrinology 2017;104(3):280-290. Epub 2016 May 11 doi: 10.1159/000446544. PMID: 27165294
Liang L, Korogi Y, Sugahara T, Ikushima I, Shigematsu Y, Okuda T, Takahashi M
Acta Radiol 2000 Nov;41(6):562-6. doi: 10.1080/028418500127345901. PMID: 11092476

Recent clinical studies

Etiology

Honegger J, Giese S, Nasi-Kordhishti I, Donegan DM
Eur J Endocrinol 2023 Feb 14;188(2) doi: 10.1093/ejendo/lvad003. PMID: 36655394
Chiloiro S, Tartaglione T, Angelini F, Bianchi A, Arena V, Giampietro A, Mormando M, Sciandra M, Laino ME, De Marinis L
Neuroendocrinology 2017;104(3):280-290. Epub 2016 May 11 doi: 10.1159/000446544. PMID: 27165294
Otake K, Takagi J
Intern Med 2003 Feb;42(2):137-8. doi: 10.2169/internalmedicine.42.137. PMID: 12636229
Ahmadi J, Meyers GS, Segall HD, Sharma OP, Hinton DR
Radiology 1995 Apr;195(1):30-4. doi: 10.1148/radiology.195.1.7892490. PMID: 7892490
Pressman EK, Zeidman SM, Reddy UM, Epstein JI, Brem H
J Reprod Med 1995 Apr;40(4):251-9. PMID: 7623353

Diagnosis

Kurokawa R, Kurokawa M, Baba A, Nakaya M, Kato S, Bapuraj J, Nakata Y, Ota Y, Srinivasan A, Abe O, Moritani T
Jpn J Radiol 2023 Sep;41(9):911-927. Epub 2023 Apr 3 doi: 10.1007/s11604-023-01417-y. PMID: 37010787Free PMC Article
Honegger J, Giese S, Nasi-Kordhishti I, Donegan DM
Eur J Endocrinol 2023 Feb 14;188(2) doi: 10.1093/ejendo/lvad003. PMID: 36655394
Donegan D, Honegger J
Endocr Pract 2022 Sep;28(9):901-910. Epub 2022 Jun 30 doi: 10.1016/j.eprac.2022.06.009. PMID: 35779833
Caranci F, Leone G, Ponsiglione A, Muto M, Tortora F, Muto M, Cirillo S, Brunese L, Cerase A
Radiol Med 2020 Mar;125(3):319-328. Epub 2019 Dec 20 doi: 10.1007/s11547-019-01120-x. PMID: 31863360
Foyouzi N
Obstet Gynecol Surv 2011 Feb;66(2):109-13. doi: 10.1097/OGX.0b013e31821d4047. PMID: 21592417

Therapy

Iwama S, Arima H
Endocr J 2020 Nov 28;67(11):1077-1083. Epub 2020 Oct 14 doi: 10.1507/endocrj.EJ20-0436. PMID: 33055452
Tebben PJ, Atkinson JL, Scheithauer BW, Erickson D
Endocr Pract 2007 Mar-Apr;13(2):169-75. doi: 10.4158/EP.13.2.169. PMID: 17490932
Otake K, Takagi J
Intern Med 2003 Feb;42(2):137-8. doi: 10.2169/internalmedicine.42.137. PMID: 12636229
Ishihara T, Hino M, Kurahachi H, Kobayashi H, Kajikawa M, Moridera K, Ikekubo K, Hattori N
Endocr J 1996 Aug;43(4):433-40. doi: 10.1507/endocrj.43.433. PMID: 8930533
Ahmadi J, Meyers GS, Segall HD, Sharma OP, Hinton DR
Radiology 1995 Apr;195(1):30-4. doi: 10.1148/radiology.195.1.7892490. PMID: 7892490

Prognosis

Caranci F, Leone G, Ponsiglione A, Muto M, Tortora F, Muto M, Cirillo S, Brunese L, Cerase A
Radiol Med 2020 Mar;125(3):319-328. Epub 2019 Dec 20 doi: 10.1007/s11547-019-01120-x. PMID: 31863360
Tartaglione T, Chiloiro S, Laino ME, Giampietro A, Gaudino S, Zoli A, Bianchi A, Pontecorvi A, Colosimo C, De Marinis L
Pituitary 2018 Aug;21(4):414-424. doi: 10.1007/s11102-018-0892-4. PMID: 29752700
Otake K, Takagi J
Intern Med 2003 Feb;42(2):137-8. doi: 10.2169/internalmedicine.42.137. PMID: 12636229
Ishihara T, Hino M, Kurahachi H, Kobayashi H, Kajikawa M, Moridera K, Ikekubo K, Hattori N
Endocr J 1996 Aug;43(4):433-40. doi: 10.1507/endocrj.43.433. PMID: 8930533
Reusch JE, Kleinschmidt-DeMasters BK, Lillehei KO, Rappe D, Gutierrez-Hartmann A
Neurosurgery 1992 Feb;30(2):268-72. doi: 10.1227/00006123-199202000-00023. PMID: 1545900

Clinical prediction guides

Donegan D, Saeed Z, Delivanis DA, Murad MH, Honegger J, Amereller F, Oguz SH, Erickson D, Bancos I
J Clin Endocrinol Metab 2022 Mar 24;107(4):1170-1190. doi: 10.1210/clinem/dgab839. PMID: 35137155Free PMC Article
Caranci F, Leone G, Ponsiglione A, Muto M, Tortora F, Muto M, Cirillo S, Brunese L, Cerase A
Radiol Med 2020 Mar;125(3):319-328. Epub 2019 Dec 20 doi: 10.1007/s11547-019-01120-x. PMID: 31863360
Tartaglione T, Chiloiro S, Laino ME, Giampietro A, Gaudino S, Zoli A, Bianchi A, Pontecorvi A, Colosimo C, De Marinis L
Pituitary 2018 Aug;21(4):414-424. doi: 10.1007/s11102-018-0892-4. PMID: 29752700
Ishihara T, Hino M, Kurahachi H, Kobayashi H, Kajikawa M, Moridera K, Ikekubo K, Hattori N
Endocr J 1996 Aug;43(4):433-40. doi: 10.1507/endocrj.43.433. PMID: 8930533
Ahmadi J, Meyers GS, Segall HD, Sharma OP, Hinton DR
Radiology 1995 Apr;195(1):30-4. doi: 10.1148/radiology.195.1.7892490. PMID: 7892490

Recent systematic reviews

Donegan D, Saeed Z, Delivanis DA, Murad MH, Honegger J, Amereller F, Oguz SH, Erickson D, Bancos I
J Clin Endocrinol Metab 2022 Mar 24;107(4):1170-1190. doi: 10.1210/clinem/dgab839. PMID: 35137155Free PMC Article

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