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Xanthogranuloma

MedGen UID:
1718640
Concept ID:
C5239388
Disease or Syndrome
Synonyms: Reactive Xanthogranuloma; xanthogranuloma
 
Monarch Initiative: MONDO:0024617

Definition

A reactive lesion characterized by the presence of a bland histiocytic cellular infiltrate admixed with giant cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVXanthogranuloma

Professional guidelines

PubMed

Giudicelli X, Rode A, Bancel B, Nguyen AT, Mabrut JY
J Visc Surg 2021 Aug;158(4):326-336. Epub 2021 Mar 23 doi: 10.1016/j.jviscsurg.2021.02.004. PMID: 33741306
Ortiz Salvador JM, Subiabre Ferrer D, Pérez Ferriols A
Actas Dermosifiliogr 2017 Jun;108(5):400-406. Epub 2017 Mar 3 doi: 10.1016/j.ad.2016.12.005. PMID: 28262109
Dalia S, Shao H, Sagatys E, Cualing H, Sokol L
Cancer Control 2014 Oct;21(4):290-300. doi: 10.1177/107327481402100405. PMID: 25310210

Recent clinical studies

Etiology

Fraitag S, Emile JF
Histopathology 2022 Jan;80(1):196-215. doi: 10.1111/his.14569. PMID: 34958507
Kemps PG, Picarsic J, Durham BH, Hélias-Rodzewicz Z, Hiemcke-Jiwa L, van den Bos C, van de Wetering MD, van Noesel CJM, van Laar JAM, Verdijk RM, Flucke UE, Hogendoorn PCW, Woei-A-Jin FJSH, Sciot R, Beilken A, Feuerhake F, Ebinger M, Möhle R, Fend F, Bornemann A, Wiegering V, Ernestus K, Méry T, Gryniewicz-Kwiatkowska O, Dembowska-Baginska B, Evseev DA, Potapenko V, Baykov VV, Gaspari S, Rossi S, Gessi M, Tamburrini G, Héritier S, Donadieu J, Bonneau-Lagacherie J, Lamaison C, Farnault L, Fraitag S, Jullié ML, Haroche J, Collin M, Allotey J, Madni M, Turner K, Picton S, Barbaro PM, Poulin A, Tam IS, El Demellawy D, Empringham B, Whitlock JA, Raghunathan A, Swanson AA, Suchi M, Brandt JM, Yaseen NR, Weinstein JL, Eldem I, Sisk BA, Sridhar V, Atkinson M, Massoth LR, Hornick JL, Alexandrescu S, Yeo KK, Petrova-Drus K, Peeke SZ, Muñoz-Arcos LS, Leino DG, Grier DD, Lorsbach R, Roy S, Kumar AR, Garg S, Tiwari N, Schafernak KT, Henry MM, van Halteren AGS, Abla O, Diamond EL, Emile JF
Blood 2022 Jan 13;139(2):256-280. doi: 10.1182/blood.2021013338. PMID: 34727172Free PMC Article
Gulati N, Allen CE
Hematol Oncol 2021 Jun;39 Suppl 1(Suppl 1):15-23. doi: 10.1002/hon.2857. PMID: 34105821Free PMC Article
Hernández-San Martín MJ, Vargas-Mora P, Aranibar L
Actas Dermosifiliogr (Engl Ed) 2020 Nov;111(9):725-733. Epub 2020 Jul 25 doi: 10.1016/j.ad.2020.07.004. PMID: 32721389
Romano RC, Fritchie KJ
Clin Lab Med 2017 Sep;37(3):603-631. Epub 2017 Jun 15 doi: 10.1016/j.cll.2017.05.007. PMID: 28802503

Diagnosis

Eckstein OS, Picarsic J, Allen CE
Pediatr Rev 2022 Oct 1;43(10):561-571. doi: 10.1542/pir.2021-005367. PMID: 36180546
Portuguese AJ, Long TH, Linenberger M
Mayo Clin Proc 2021 Sep;96(9):2432-2434. doi: 10.1016/j.mayocp.2021.05.012. PMID: 34481598
Hernández-San Martín MJ, Vargas-Mora P, Aranibar L
Actas Dermosifiliogr (Engl Ed) 2020 Nov;111(9):725-733. Epub 2020 Jul 25 doi: 10.1016/j.ad.2020.07.004. PMID: 32721389
Hernandez-Martin A, Baselga E, Drolet BA, Esterly NB
J Am Acad Dermatol 1997 Mar;36(3 Pt 1):355-67; quiz 368-9. doi: 10.1016/s0190-9622(97)80207-1. PMID: 9091465
van Hellenberg Hubar JL, Joosten EM, Wevers RA
Clin Neurol Neurosurg 1992;94 Suppl:S165-7. doi: 10.1016/0303-8467(92)90059-c. PMID: 1320501

Therapy

Steinhelfer L, Kühnel T, Jägle H, Mayer S, Karrer S, Haubner F, Schreml S
Orphanet J Rare Dis 2022 Mar 24;17(1):132. doi: 10.1186/s13023-022-02291-z. PMID: 35331271Free PMC Article
Kemps PG, Picarsic J, Durham BH, Hélias-Rodzewicz Z, Hiemcke-Jiwa L, van den Bos C, van de Wetering MD, van Noesel CJM, van Laar JAM, Verdijk RM, Flucke UE, Hogendoorn PCW, Woei-A-Jin FJSH, Sciot R, Beilken A, Feuerhake F, Ebinger M, Möhle R, Fend F, Bornemann A, Wiegering V, Ernestus K, Méry T, Gryniewicz-Kwiatkowska O, Dembowska-Baginska B, Evseev DA, Potapenko V, Baykov VV, Gaspari S, Rossi S, Gessi M, Tamburrini G, Héritier S, Donadieu J, Bonneau-Lagacherie J, Lamaison C, Farnault L, Fraitag S, Jullié ML, Haroche J, Collin M, Allotey J, Madni M, Turner K, Picton S, Barbaro PM, Poulin A, Tam IS, El Demellawy D, Empringham B, Whitlock JA, Raghunathan A, Swanson AA, Suchi M, Brandt JM, Yaseen NR, Weinstein JL, Eldem I, Sisk BA, Sridhar V, Atkinson M, Massoth LR, Hornick JL, Alexandrescu S, Yeo KK, Petrova-Drus K, Peeke SZ, Muñoz-Arcos LS, Leino DG, Grier DD, Lorsbach R, Roy S, Kumar AR, Garg S, Tiwari N, Schafernak KT, Henry MM, van Halteren AGS, Abla O, Diamond EL, Emile JF
Blood 2022 Jan 13;139(2):256-280. doi: 10.1182/blood.2021013338. PMID: 34727172Free PMC Article
Portuguese AJ, Long TH, Linenberger M
Mayo Clin Proc 2021 Sep;96(9):2432-2434. doi: 10.1016/j.mayocp.2021.05.012. PMID: 34481598
Dellatorre G, Miqueloto JK
JAMA Dermatol 2020 Jun 1;156(6):696. doi: 10.1001/jamadermatol.2020.0897. PMID: 32374351
Cadera W, Silver MM, Burt L
Can J Ophthalmol 1983 Jun;18(4):169-74. PMID: 6192889

Prognosis

Pan Z, Xu ML
Surg Pathol Clin 2019 Sep;12(3):805-829. Epub 2019 Jun 8 doi: 10.1016/j.path.2019.03.013. PMID: 31352989
Ranganathan S
Semin Diagn Pathol 2016 Nov;33(6):396-409. Epub 2016 Sep 1 doi: 10.1053/j.semdp.2016.08.009. PMID: 27720561
Read RW, Zamir E, Rao NA
Surv Ophthalmol 2002 Mar-Apr;47(2):81-124. doi: 10.1016/s0039-6257(01)00305-8. PMID: 11918892
Mehregan DA, Winkelmann RK
Arch Dermatol 1992 Jan;128(1):94-100. PMID: 1739294
Ringel E, Moschella S
Arch Dermatol 1985 Dec;121(12):1531-41. PMID: 2998286

Clinical prediction guides

Kemps PG, Picarsic J, Durham BH, Hélias-Rodzewicz Z, Hiemcke-Jiwa L, van den Bos C, van de Wetering MD, van Noesel CJM, van Laar JAM, Verdijk RM, Flucke UE, Hogendoorn PCW, Woei-A-Jin FJSH, Sciot R, Beilken A, Feuerhake F, Ebinger M, Möhle R, Fend F, Bornemann A, Wiegering V, Ernestus K, Méry T, Gryniewicz-Kwiatkowska O, Dembowska-Baginska B, Evseev DA, Potapenko V, Baykov VV, Gaspari S, Rossi S, Gessi M, Tamburrini G, Héritier S, Donadieu J, Bonneau-Lagacherie J, Lamaison C, Farnault L, Fraitag S, Jullié ML, Haroche J, Collin M, Allotey J, Madni M, Turner K, Picton S, Barbaro PM, Poulin A, Tam IS, El Demellawy D, Empringham B, Whitlock JA, Raghunathan A, Swanson AA, Suchi M, Brandt JM, Yaseen NR, Weinstein JL, Eldem I, Sisk BA, Sridhar V, Atkinson M, Massoth LR, Hornick JL, Alexandrescu S, Yeo KK, Petrova-Drus K, Peeke SZ, Muñoz-Arcos LS, Leino DG, Grier DD, Lorsbach R, Roy S, Kumar AR, Garg S, Tiwari N, Schafernak KT, Henry MM, van Halteren AGS, Abla O, Diamond EL, Emile JF
Blood 2022 Jan 13;139(2):256-280. doi: 10.1182/blood.2021013338. PMID: 34727172Free PMC Article
Peruilh-Bagolini L, Silva-Astorga M, Hernández San Martín MJ, Manoli MS, Papageorgiou C, Apalla Z, Lallas A
Dermatology 2021;237(6):946-951. Epub 2020 Oct 19 doi: 10.1159/000510265. PMID: 33075787
Schmitt A, Volz A
J Dtsch Dermatol Ges 2019 May;17(5):518-533. doi: 10.1111/ddg.13848. PMID: 31115996
Fernández-Herrera J, Pedraz J
Semin Cutan Med Surg 2007 Jun;26(2):108-13. doi: 10.1016/j.sder.2007.02.008. PMID: 17544963
Cadera W, Silver MM, Burt L
Can J Ophthalmol 1983 Jun;18(4):169-74. PMID: 6192889

Recent systematic reviews

Zou T, Wei A, Ma H, Lian H, Liu Y, Wang D, Zhao Y, Cui L, Li Z, Zhang R, Wang T
Pediatr Blood Cancer 2023 May;70(5):e30232. Epub 2023 Feb 13 doi: 10.1002/pbc.30232. PMID: 36779547
Steinhelfer L, Kühnel T, Jägle H, Mayer S, Karrer S, Haubner F, Schreml S
Orphanet J Rare Dis 2022 Mar 24;17(1):132. doi: 10.1186/s13023-022-02291-z. PMID: 35331271Free PMC Article
Nelson CA, Zhong CS, Hashemi DA, Ashchyan HJ, Brown-Joel Z, Noe MH, Imadojemu S, Micheletti RG, Vleugels RA, Wanat KA, Rosenbach M, Mostaghimi A
JAMA Dermatol 2020 Mar 1;156(3):270-279. doi: 10.1001/jamadermatol.2019.4221. PMID: 31940000Free PMC Article
Miguel D, Lukacs J, Illing T, Elsner P
J Eur Acad Dermatol Venereol 2017 Feb;31(2):221-235. Epub 2016 Jul 19 doi: 10.1111/jdv.13786. PMID: 27436448
Zvulunov A, Barak Y, Metzker A
Arch Dermatol 1995 Aug;131(8):904-8. PMID: 7632061

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