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Pulmonary artery leiomyosarcoma

MedGen UID:
233372
•Concept ID:
C1335572
•
Neoplastic Process
Synonyms: Leiomyosarcoma of Pulmonary Artery; leiomyosarcoma of pulmonary artery; Leiomyosarcoma of the Pulmonary Artery; leiomyosarcoma of the pulmonary artery; Pulmonary Artery Leiomyosarcoma; pulmonary artery leiomyosarcoma
 
Monarch Initiative: MONDO:0004207

Definition

An aggressive malignant smooth muscle neoplasm, arising from the pulmonary artery It is characterized by a proliferation of neoplastic spindle cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPulmonary artery leiomyosarcoma

Professional guidelines

PubMed

Surgical treatment of pulmonary artery sarcoma.
Mayer E, Kriegsmann J, Gaumann A, Kauczor HU, Dahm M, Hake U, Schmid FX, Oelert H
J Thorac Cardiovasc Surg 2001 Jan;121(1):77-82. doi: 10.1067/mtc.2001.111423. PMID: 11135162
Surgical treatment of primary pulmonary sarcomas.
Bacha EA, Wright CD, Grillo HC, Wain JC, Moncure A, Keel SB, Donahue DM, Mathisen DJ
Eur J Cardiothorac Surg 1999 Apr;15(4):456-60. doi: 10.1016/s1010-7940(99)00045-7. PMID: 10371121

Recent clinical studies

Diagnosis

A Rare Case of Pulmonary Leiomyosarcoma.
He J, Tang Y, Zhao F, Zheng B, Tang S, Gong J, Wang L, Zhou Y
Acta Med Indones 2023 Jan;55(1):83-86. PMID: 36999261
Pulmonary artery leiomyosarcoma: an unusual cause of shortness of breath.
Flaherty G, McCarthy P, Mortimer G
Ir J Med Sci 2011 Mar;180(1):275-8. Epub 2009 Nov 17 doi: 10.1007/s11845-009-0451-0. PMID: 19921308
Thromboembolism in pulmonary artery sarcoma.
Farsad M, Pernter P, Triani A, Osele L, Wiedermann CJ
Clin Nucl Med 2009 Apr;34(4):239-40. doi: 10.1097/RLU.0b013e31819a1f7b. PMID: 19300057
Primary pulmonary artery leiomyosarcoma.
Croitoru AG, Klein MJ, Galla JD, Fallon JT
Cardiovasc Pathol 2003 May-Jun;12(3):166-9. doi: 10.1016/s1054-8807(02)00184-9. PMID: 12763557
Pulmonary artery leiomyosarcoma.
Chan SH, Tsai LM, Tsai WC, Li YH, Chen JH, Luo CY
J Formos Med Assoc 1999 Aug;98(8):578-81. PMID: 10502913

Therapy

Primary leiomyosarcoma of the pulmonary artery confirmed by catheter suction biopsy.
Yamada N, Kamei S, Yasuda F, Isaka N, Yada I, Nakano T
Chest 1998 Feb;113(2):555-6. doi: 10.1378/chest.113.2.555. PMID: 9498986

Prognosis

Pulmonary artery leiomyosarcoma: an unusual cause of shortness of breath.
Flaherty G, McCarthy P, Mortimer G
Ir J Med Sci 2011 Mar;180(1):275-8. Epub 2009 Nov 17 doi: 10.1007/s11845-009-0451-0. PMID: 19921308
Pulmonary artery leiomyosarcoma expressing Epstein-Barr virus in an immunocompetent individual.
Yokoi S, Iizasa T, Hiroshima K, Saitoh Y, Fujisawa T
Ann Thorac Surg 2006 May;81(5):1897-9. doi: 10.1016/j.athoracsur.2005.05.083. PMID: 16631703
Pulmonary artery leiomyosarcoma with thyroid metastases.
D'Andrea N, Romano V, Mattioli F, Candia S, Montanari A, Guidi L, Carvalho M, Sanguinetti CM
Monaldi Arch Chest Dis 2003 Oct-Dec;59(4):304-7. PMID: 15148841

Clinical prediction guides

An autopsy case of pulmonary artery leiomyosarcoma.
Nakazawa K, Itoh N, Shigematsu H, Kanbayasi T
Acta Pathol Jpn 1993 Jan-Feb;43(1-2):76-81. doi: 10.1111/j.1440-1827.1993.tb02918.x. PMID: 8465660

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