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Intermediate Fibroblastic Neoplasm

MedGen UID:
233565
Concept ID:
C1334212
Neoplastic Process
Synonyms: Intermediate Fibroblastic Tumor; Intermediate Fibrocytic Neoplasm; Intermediate Fibrocytic Tumor; Intermediate Fibrogenic Neoplasm; Intermediate Fibrogenic Tumor; Intermediate Fibrous Neoplasm; Intermediate Fibrous Tumor

Definition

A locally aggressive or rarely metastasizing neoplasm that arises from the soft tissues. It is characterized by the presence of neoplastic spindle-shaped fibroblasts. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIntermediate Fibroblastic Neoplasm

Professional guidelines

PubMed

Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Demicco EG, Wagner MJ, Maki RG, Gupta V, Iofin I, Lazar AJ, Wang WL
Mod Pathol 2017 Oct;30(10):1433-1442. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.54. PMID: 28731041
Demicco EG, Park MS, Araujo DM, Fox PS, Bassett RL, Pollock RE, Lazar AJ, Wang WL
Mod Pathol 2012 Sep;25(9):1298-306. Epub 2012 May 11 doi: 10.1038/modpathol.2012.83. PMID: 22575866

Recent clinical studies

Etiology

Haseli S, Mansoori B, Christensen D, Abadi A, Pooyan A, Shomal Zadeh F, Mau B, Khalili N, Murphey M, Chalian M
Radiographics 2023 Aug;43(8):e230005. doi: 10.1148/rg.230005. PMID: 37440448
Kasper B
Curr Opin Oncol 2023 Jul 1;35(4):292-295. Epub 2023 May 3 doi: 10.1097/CCO.0000000000000953. PMID: 37222208
Demicco EG, Wagner MJ, Maki RG, Gupta V, Iofin I, Lazar AJ, Wang WL
Mod Pathol 2017 Oct;30(10):1433-1442. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.54. PMID: 28731041
Demicco EG, Park MS, Araujo DM, Fox PS, Bassett RL, Pollock RE, Lazar AJ, Wang WL
Mod Pathol 2012 Sep;25(9):1298-306. Epub 2012 May 11 doi: 10.1038/modpathol.2012.83. PMID: 22575866
Coffin CM, Alaggio R
Pediatr Dev Pathol 2012;15(1 Suppl):127-80. doi: 10.2350/10-12-0944-PB.1. PMID: 22420727

Diagnosis

Perret R, Hostein I
Surg Pathol Clin 2024 Mar;17(1):1-12. Epub 2023 Aug 1 doi: 10.1016/j.path.2023.06.001. PMID: 38278599
Marini F, Giusti F, Iantomasi T, Brandi ML
Int J Mol Sci 2021 Oct 18;22(20) doi: 10.3390/ijms222011206. PMID: 34681865Free PMC Article
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Surabhi VR, Chua S, Patel RP, Takahashi N, Lalwani N, Prasad SR
Radiol Clin North Am 2016 May;54(3):553-63. Epub 2016 Mar 12 doi: 10.1016/j.rcl.2015.12.005. PMID: 27153788
Fisher C
Adv Anat Pathol 2004 Jul;11(4):190-201. doi: 10.1097/01.pap.0000131773.16130.aa. PMID: 15220822

Therapy

Kornreich L, Orbach D, Nicolas N, Brisse HJ, Berlanga P, Defachelles AS, Mansuy L, Verite C, Saumet L, Karanian M, Corradini N
Tumori 2023 Oct;109(5):511-518. Epub 2023 Apr 28 doi: 10.1177/03008916231169806. PMID: 37114926
Zhao M, He H, Cao D, Fan D, Xu M, Zhang X, Ru G
Am J Clin Pathol 2022 Jul 1;158(1):35-46. doi: 10.1093/ajcp/aqab211. PMID: 34999741
Chen T, Wang Y, Goetz L, Corey Z, Dougher MC, Smith JD, Fox EJ, Freiberg AS, Flemming D, Fanburg-Smith JC
Ann Diagn Pathol 2021 Oct;54:151800. Epub 2021 Jul 22 doi: 10.1016/j.anndiagpath.2021.151800. PMID: 34464935
Kasper B, Raut CP, Gronchi A
Cancer 2020 Dec 15;126(24):5213-5221. Epub 2020 Oct 6 doi: 10.1002/cncr.33233. PMID: 33022074
Gounder MM, Thomas DM, Tap WD
J Clin Oncol 2018 Jan 10;36(2):202-209. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.8482. PMID: 29220303Free PMC Article

Prognosis

Perret R, Hostein I
Surg Pathol Clin 2024 Mar;17(1):1-12. Epub 2023 Aug 1 doi: 10.1016/j.path.2023.06.001. PMID: 38278599
Kasper B
Curr Opin Oncol 2023 Jul 1;35(4):292-295. Epub 2023 May 3 doi: 10.1097/CCO.0000000000000953. PMID: 37222208
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Demicco EG, Wagner MJ, Maki RG, Gupta V, Iofin I, Lazar AJ, Wang WL
Mod Pathol 2017 Oct;30(10):1433-1442. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.54. PMID: 28731041
Demicco EG, Park MS, Araujo DM, Fox PS, Bassett RL, Pollock RE, Lazar AJ, Wang WL
Mod Pathol 2012 Sep;25(9):1298-306. Epub 2012 May 11 doi: 10.1038/modpathol.2012.83. PMID: 22575866

Clinical prediction guides

Haseli S, Mansoori B, Christensen D, Abadi A, Pooyan A, Shomal Zadeh F, Mau B, Khalili N, Murphey M, Chalian M
Radiographics 2023 Aug;43(8):e230005. doi: 10.1148/rg.230005. PMID: 37440448
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Gounder MM, Thomas DM, Tap WD
J Clin Oncol 2018 Jan 10;36(2):202-209. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.8482. PMID: 29220303Free PMC Article
Demicco EG, Wagner MJ, Maki RG, Gupta V, Iofin I, Lazar AJ, Wang WL
Mod Pathol 2017 Oct;30(10):1433-1442. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.54. PMID: 28731041
Demicco EG, Park MS, Araujo DM, Fox PS, Bassett RL, Pollock RE, Lazar AJ, Wang WL
Mod Pathol 2012 Sep;25(9):1298-306. Epub 2012 May 11 doi: 10.1038/modpathol.2012.83. PMID: 22575866

Recent systematic reviews

Titsinides S, Nikitakis NG, Tasoulas J, Daskalopoulos A, Goutzanis L, Sklavounou A
Int J Surg Pathol 2017 Sep;25(6):526-532. Epub 2017 Apr 24 doi: 10.1177/1066896917705197. PMID: 28436288

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