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Pulmonary vein leiomyosarcoma

MedGen UID:
235513
•Concept ID:
C1335575
•
Neoplastic Process
Synonyms: Leiomyosarcoma of Pulmonary Vein; leiomyosarcoma of pulmonary vein; Leiomyosarcoma of the Pulmonary Vein; leiomyosarcoma of the pulmonary vein; Pulmonary Vein Leiomyosarcoma; pulmonary vein leiomyosarcoma
 
Monarch Initiative: MONDO:0004206

Definition

An aggressive malignant smooth muscle neoplasm, arising from the pulmonary vein. It is characterized by a proliferation of neoplastic spindle cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPulmonary vein leiomyosarcoma

Professional guidelines

PubMed

Surgical treatment of primary pulmonary sarcomas.
Bacha EA, Wright CD, Grillo HC, Wain JC, Moncure A, Keel SB, Donahue DM, Mathisen DJ
Eur J Cardiothorac Surg 1999 Apr;15(4):456-60. doi: 10.1016/s1010-7940(99)00045-7. PMID: 10371121

Recent clinical studies

Diagnosis

Sarcomas: rare primary malignant tumors of the thorax.
Cakir O, Topal U, Bayram AS, Tolunay S
Diagn Interv Radiol 2005 Mar;11(1):23-7. PMID: 15795839
Unusual pulmonary lesions: case 3. Pulmonary vein leiomyosarcoma presenting as a left atrial mass.
Laroia ST, Potti A, Rabbani M, Mehdi SA, Koch M
J Clin Oncol 2002 Jun 1;20(11):2749-51. doi: 10.1200/JCO.2002.20.11.2749. PMID: 12039939

Therapy

Straight to the heart: pulmonary vein leiomyosarcoma.
Patel SM, Kadakia KC, Maleszewski JJ, Marks RS
Am J Med 2013 Feb;126(2):117-9. doi: 10.1016/j.amjmed.2012.11.002. PMID: 23331438

Prognosis

Straight to the heart: pulmonary vein leiomyosarcoma.
Patel SM, Kadakia KC, Maleszewski JJ, Marks RS
Am J Med 2013 Feb;126(2):117-9. doi: 10.1016/j.amjmed.2012.11.002. PMID: 23331438

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