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Vasculitis, lymphocytic, nodular

MedGen UID:
348635
Concept ID:
C1860519
Disease or Syndrome
Synonym: Lymphocytic vasculitis
 
Monarch Initiative: MONDO:0008640
OMIM®: 192310

Definition

Lymphocytic vasculitis is one of several skin conditions which are collectively referred to as cutaneous vasculitis. In lymphocytic vasculitis, white blood cells (lymphocytes) cause damage to blood vessels in the skin. This condition is thought to be caused by a number of factors, but the exact cause of most cases is not known. This disease can present with a variety of symptoms, depending on the size, location, and severity of the affected area. In a minority of patients, cutaneous vasculitis can be part of a more severe vasculitis affecting other organs in the body - this is known as systemic vasculitis. [from MONDO]

Clinical features

From HPO
Nodular inflammatory vasculitis
MedGen UID:
870762
Concept ID:
C4025219
Disease or Syndrome
Abnormality of metabolism/homeostasis
MedGen UID:
867398
Concept ID:
C4021768
Finding

Recent clinical studies

Etiology

Favetti F, Mazzotta G, Papalia M, Panegrossi G, Casella F, Falez F
Eur Rev Med Pharmacol Sci 2019 Apr;23(2 Suppl):86-93. doi: 10.26355/eurrev_201904_17478. PMID: 30977875
Nawabi DH, Nassif NA, Do HT, Stoner K, Elpers M, Su EP, Wright T, Potter HG, Padgett DE
Clin Orthop Relat Res 2014 Feb;472(2):543-54. doi: 10.1007/s11999-013-3199-9. PMID: 23897506Free PMC Article
Nawabi DH, Gold S, Lyman S, Fields K, Padgett DE, Potter HG
Clin Orthop Relat Res 2014 Feb;472(2):471-81. doi: 10.1007/s11999-013-2788-y. PMID: 23354460Free PMC Article
Minor DR, Bunker SR, Doyle J
J Clin Oncol 2013 Jul 10;31(20):e356. Epub 2013 Jun 3 doi: 10.1200/JCO.2012.47.5095. PMID: 23733772

Diagnosis

Nawabi DH, Gold S, Lyman S, Fields K, Padgett DE, Potter HG
Clin Orthop Relat Res 2014 Feb;472(2):471-81. doi: 10.1007/s11999-013-2788-y. PMID: 23354460Free PMC Article
Duggan PJ, Burke CJ, Saha S, Moonim M, George M, Desai A, Houghton R
Clin Radiol 2013 Nov;68(11):1089-96. Epub 2013 Aug 6 doi: 10.1016/j.crad.2013.04.017. PMID: 23932675

Therapy

Favetti F, Mazzotta G, Papalia M, Panegrossi G, Casella F, Falez F
Eur Rev Med Pharmacol Sci 2019 Apr;23(2 Suppl):86-93. doi: 10.26355/eurrev_201904_17478. PMID: 30977875
Nawabi DH, Nassif NA, Do HT, Stoner K, Elpers M, Su EP, Wright T, Potter HG, Padgett DE
Clin Orthop Relat Res 2014 Feb;472(2):543-54. doi: 10.1007/s11999-013-3199-9. PMID: 23897506Free PMC Article
Nawabi DH, Gold S, Lyman S, Fields K, Padgett DE, Potter HG
Clin Orthop Relat Res 2014 Feb;472(2):471-81. doi: 10.1007/s11999-013-2788-y. PMID: 23354460Free PMC Article
Duggan PJ, Burke CJ, Saha S, Moonim M, George M, Desai A, Houghton R
Clin Radiol 2013 Nov;68(11):1089-96. Epub 2013 Aug 6 doi: 10.1016/j.crad.2013.04.017. PMID: 23932675
Minor DR, Bunker SR, Doyle J
J Clin Oncol 2013 Jul 10;31(20):e356. Epub 2013 Jun 3 doi: 10.1200/JCO.2012.47.5095. PMID: 23733772

Prognosis

Nawabi DH, Nassif NA, Do HT, Stoner K, Elpers M, Su EP, Wright T, Potter HG, Padgett DE
Clin Orthop Relat Res 2014 Feb;472(2):543-54. doi: 10.1007/s11999-013-3199-9. PMID: 23897506Free PMC Article
Nawabi DH, Gold S, Lyman S, Fields K, Padgett DE, Potter HG
Clin Orthop Relat Res 2014 Feb;472(2):471-81. doi: 10.1007/s11999-013-2788-y. PMID: 23354460Free PMC Article
Minor DR, Bunker SR, Doyle J
J Clin Oncol 2013 Jul 10;31(20):e356. Epub 2013 Jun 3 doi: 10.1200/JCO.2012.47.5095. PMID: 23733772
Wiley KF, Ding K, Stoner JA, Teague DC, Yousuf KM
J Arthroplasty 2013 Aug;28(7):1238-45. Epub 2013 May 6 doi: 10.1016/j.arth.2013.03.027. PMID: 23660012

Clinical prediction guides

Nawabi DH, Nassif NA, Do HT, Stoner K, Elpers M, Su EP, Wright T, Potter HG, Padgett DE
Clin Orthop Relat Res 2014 Feb;472(2):543-54. doi: 10.1007/s11999-013-3199-9. PMID: 23897506Free PMC Article
Nawabi DH, Gold S, Lyman S, Fields K, Padgett DE, Potter HG
Clin Orthop Relat Res 2014 Feb;472(2):471-81. doi: 10.1007/s11999-013-2788-y. PMID: 23354460Free PMC Article

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