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Nodular inflammatory vasculitis

MedGen UID:
870762
Concept ID:
C4025219
Disease or Syndrome
HPO: HP:0005300

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNodular inflammatory vasculitis

Conditions with this feature

Vasculitis, lymphocytic, nodular
MedGen UID:
348635
Concept ID:
C1860519
Disease or Syndrome
Lymphocytic vasculitis is one of several skin conditions which are collectively referred to as cutaneous vasculitis. In lymphocytic vasculitis, white blood cells (lymphocytes) cause damage to blood vessels in the skin. This condition is thought to be caused by a number of factors, but the exact cause of most cases is not known. This disease can present with a variety of symptoms, depending on the size, location, and severity of the affected area. In a minority of patients, cutaneous vasculitis can be part of a more severe vasculitis affecting other organs in the body - this is known as systemic vasculitis.

Professional guidelines

PubMed

Watson P, Romano A
Eye (Lond) 2014 Aug;28(8):915-30. Epub 2014 May 30 doi: 10.1038/eye.2014.110. PMID: 24875228Free PMC Article
Borroni G, Giorgini C, Tomasini C, Brazzelli V
G Ital Dermatol Venereol 2013 Aug;148(4):325-33. PMID: 23900156
Gilchrist H, Patterson JW
Dermatol Ther 2010 Jul-Aug;23(4):320-7. doi: 10.1111/j.1529-8019.2010.01332.x. PMID: 20666819

Recent clinical studies

Etiology

Gales L, Cribier B, Lipsker D, Lenormand C
J Eur Acad Dermatol Venereol 2023 Feb;37(2):436-442. Epub 2022 Oct 17 doi: 10.1111/jdv.18630. PMID: 36178454
Abd El Latif E, Seleet MM, El Hennawi H, Abdulbadiea Rashed M, Elbarbary H, Sabry K, Abdelmonagy Ibrahim M
Ocul Immunol Inflamm 2019;27(6):890-896. Epub 2018 Nov 9 doi: 10.1080/09273948.2018.1544372. PMID: 30412434
Ferrara G, Stefanato CM, Gianotti R, Kubba A, Annessi G
G Ital Dermatol Venereol 2013 Aug;148(4):387-94. PMID: 23900160
Chen KR, Carlson JA
Am J Clin Dermatol 2008;9(2):71-92. doi: 10.2165/00128071-200809020-00001. PMID: 18284262
Sabaté JM, Clotet M, Gómez A, De Las Heras P, Torrubia S, Salinas T
Radiographics 2005 Mar-Apr;25(2):411-24. doi: 10.1148/rg.252045077. PMID: 15798059

Diagnosis

Saha BK, Dawani O, Chong WH, Bonnier A
Am J Med Sci 2022 Feb;363(2):191-198. Epub 2022 Jan 2 doi: 10.1016/j.amjms.2021.08.010. PMID: 34986366
Ferrara G, Stefanato CM, Gianotti R, Kubba A, Annessi G
G Ital Dermatol Venereol 2013 Aug;148(4):387-94. PMID: 23900160
Ramdial PK, Naidoo DK
J Clin Pathol 2009 Jun;62(6):493-504. Epub 2009 Jan 20 doi: 10.1136/jcp.2008.058289. PMID: 19155238
Ter Poorten MC, Thiers BH
Dermatol Clin 2002 Jul;20(3):421-33, vi. doi: 10.1016/s0733-8635(02)00008-6. PMID: 12170876
Requena L, Requena C
Dermatol Online J 2002 Jun;8(1):4. PMID: 12165214

Therapy

Valerio L, Baddour LM
Semin Thromb Hemost 2023 Nov;49(8):840-847. Epub 2022 Nov 23 doi: 10.1055/s-0042-1758742. PMID: 36417928
Eze JN, Odimegwu CL, Okafor OC, Nwafia IN
Niger J Clin Pract 2022 Sep;25(9):1611-1614. doi: 10.4103/njcp.njcp_348_22. PMID: 36149228
Gremese E, Alivernini S, Tolusso B, Zeidler MP, Ferraccioli G
J Leukoc Biol 2019 Nov;106(5):1063-1068. Epub 2019 Jul 16 doi: 10.1002/JLB.5RU0519-145R. PMID: 31313387Free PMC Article
Gilchrist H, Patterson JW
Dermatol Ther 2010 Jul-Aug;23(4):320-7. doi: 10.1111/j.1529-8019.2010.01332.x. PMID: 20666819
Chen KR, Carlson JA
Am J Clin Dermatol 2008;9(2):71-92. doi: 10.2165/00128071-200809020-00001. PMID: 18284262

Prognosis

Ramdial PK, Naidoo DK
J Clin Pathol 2009 Jun;62(6):493-504. Epub 2009 Jan 20 doi: 10.1136/jcp.2008.058289. PMID: 19155238
Chen KR, Carlson JA
Am J Clin Dermatol 2008;9(2):71-92. doi: 10.2165/00128071-200809020-00001. PMID: 18284262
Requena L, Sánchez Yus E
Semin Cutan Med Surg 2007 Jun;26(2):114-25. doi: 10.1016/j.sder.2007.02.009. PMID: 17544964
Díaz-Pérez JL, De Lagrán ZM, Díaz-Ramón JL, Winkelmann RK
Semin Cutan Med Surg 2007 Jun;26(2):77-86. doi: 10.1016/j.sder.2007.02.003. PMID: 17544958
Requena L, Requena C
Dermatol Online J 2002 Jun;8(1):4. PMID: 12165214

Clinical prediction guides

Brix SR, Noriega M, Herden EM, Goldmann B, Langbehn U, Busch M, Jabs WJ, Steinmetz OM, Panzer U, Huber TB, Stahl RAK, Wiech T
Histopathology 2018 Jun;72(7):1093-1101. Epub 2018 Mar 25 doi: 10.1111/his.13487. PMID: 29453894
Watson P, Romano A
Eye (Lond) 2014 Aug;28(8):915-30. Epub 2014 May 30 doi: 10.1038/eye.2014.110. PMID: 24875228Free PMC Article
Kuijpers TW, Biezeveld M, Achterhuis A, Kuipers I, Lam J, Hack CE, Becker AE, van der Wal AC
Pediatrics 2003 Oct;112(4):986-92. doi: 10.1542/peds.112.4.986. PMID: 14523200
Walker NJ, Zurier RB
Clin Liver Dis 2002 Nov;6(4):933-46. doi: 10.1016/s1089-3261(02)00052-1. PMID: 12516200
Hotchi M
Heart Vessels Suppl 1992;7:11-7. doi: 10.1007/BF01744538. PMID: 1360954

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