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Anomalous origin of coronary artery from the pulmonary artery

MedGen UID:
868842
Concept ID:
C4023252
Anatomical Abnormality
HPO: HP:0011637

Definition

A coronary artery begins (branches off from) the pulmonary artery rather than as normal from the root of the aorta. [from HPO]

Professional guidelines

PubMed

Kanagala SG, Gupta V, Dunn GV, Kaur H, Zieneddine F, Jain R, Garg N
Curr Cardiol Rev 2023;19(6):50-55. doi: 10.2174/1573403X19666230530095341. PMID: 37259216Free PMC Article
Dali W, Tlili R, Ben Slima H, Naccache S, Mbarek D, Boujnah MR
Tunis Med 2019 Feb;97(2):365-372. PMID: 31539096
Boris JR, Brothers JA
Cardiol Young 2015 Dec;25(8):1540-5. doi: 10.1017/S1047951115002127. PMID: 26675602

Recent clinical studies

Etiology

Cashen K, Kwiatkowski DM, Riley CM, Buckley J, Sassalos P, Gowda KN, Iliopoulos I, Bakar A, Chiwane S, Badheka A, Moser EAS, Mastropietro CW; Collaborative Research from the Pediatric Cardiac Intensive Care Society (CoRe-PCICS) Investigators
Pediatr Crit Care Med 2021 Dec 1;22(12):e626-e635. doi: 10.1097/PCC.0000000000002820. PMID: 34432672
Ojha V, Pandey NN, Kumar S, Ramakrishnan S, Jagia P
J Card Surg 2021 Nov;36(11):4043-4053. Epub 2021 Aug 19 doi: 10.1111/jocs.15926. PMID: 34414605
Goo HW
Korean J Radiol 2021 Sep;22(9):1441-1450. Epub 2021 May 20 doi: 10.3348/kjr.2021.0034. PMID: 34047508Free PMC Article
Wu LP, Zhang YQ, Chen LJ, Liu YQ
J Med Ultrason (2001) 2019 Jul;46(3):335-341. Epub 2019 Feb 21 doi: 10.1007/s10396-019-00933-7. PMID: 30790093
Yuan SM
Rev Bras Cir Cardiovasc 2014 Oct-Dec;29(4):622-9. doi: 10.5935/1678-9741.20140109. PMID: 25714217Free PMC Article

Diagnosis

Guenther TM, Chen SA, Gustafson JD, Ing FF, Brothers JA, Raff GW
Cardiol Young 2021 Oct;31(10):1563-1570. Epub 2021 Jul 26 doi: 10.1017/S1047951121002997. PMID: 34304753
Goo HW
Korean J Radiol 2021 Sep;22(9):1441-1450. Epub 2021 May 20 doi: 10.3348/kjr.2021.0034. PMID: 34047508Free PMC Article
Guenther TM, Sherazee EA, Wisneski AD, Gustafson JD, Wozniak CJ, Raff GW
Ann Thorac Surg 2020 Sep;110(3):1063-1071. Epub 2020 Mar 7 doi: 10.1016/j.athoracsur.2020.01.082. PMID: 32156586
Wu LP, Zhang YQ, Chen LJ, Liu YQ
J Med Ultrason (2001) 2019 Jul;46(3):335-341. Epub 2019 Feb 21 doi: 10.1007/s10396-019-00933-7. PMID: 30790093
Silverman NH
Cardiol Young 2015 Dec;25(8):1512-23. doi: 10.1017/S1047951115002565. PMID: 26675598

Therapy

Chua F, Vongbunyong K, Urgun DA, Ghashghaei R
BMC Cardiovasc Disord 2023 Dec 14;23(1):618. doi: 10.1186/s12872-023-03616-x. PMID: 38097961Free PMC Article
Goerne H, de la Fuente D, Cabrera M, Chaturvedi A, Vargas D, Young PM, Saboo SS, Rajiah P
Radiographics 2021 May-Jun;41(3):699-719. Epub 2021 Apr 2 doi: 10.1148/rg.2021200147. PMID: 33798007
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Hoffman JI
Cardiol Young 2014 Oct;24(5):774-91. Epub 2014 Apr 23 doi: 10.1017/S1047951114000250. PMID: 24758740
Kazmierczak PA, Ostrowska K, Dryzek P, Moll JA, Moll JJ
Interact Cardiovasc Thorac Surg 2013 Jun;16(6):797-801. Epub 2013 Feb 26 doi: 10.1093/icvts/ivt061. PMID: 23442939Free PMC Article

Prognosis

Beyaz MO, Coban S, Ulukan MO, Dogan MS, Erol C, Saritas T, Erdem A, Akdeniz C, Ugurlucan M, Akcevin A, Turkoglu H
Heart Surg Forum 2021 Jan 20;24(1):E065-E071. doi: 10.1532/hsf.3421. PMID: 33635248
Yuan XC, Hu J, Zeng X, Zhou AY, Chen L
Medicine (Baltimore) 2019 Nov;98(47):e18046. doi: 10.1097/MD.0000000000018046. PMID: 31764828Free PMC Article
Silva A, Baptista MJ, Araújo E
Rev Port Cardiol (Engl Ed) 2018 Apr;37(4):341-350. Epub 2018 Feb 26 doi: 10.1016/j.repc.2017.09.015. PMID: 29496389
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Hoffman JI
Cardiol Young 2014 Oct;24(5):774-91. Epub 2014 Apr 23 doi: 10.1017/S1047951114000250. PMID: 24758740

Clinical prediction guides

Chua F, Vongbunyong K, Urgun DA, Ghashghaei R
BMC Cardiovasc Disord 2023 Dec 14;23(1):618. doi: 10.1186/s12872-023-03616-x. PMID: 38097961Free PMC Article
Kanagala SG, Gupta V, Dunn GV, Kaur H, Zieneddine F, Jain R, Garg N
Curr Cardiol Rev 2023;19(6):50-55. doi: 10.2174/1573403X19666230530095341. PMID: 37259216Free PMC Article
Feng T, Zhangke G, Song B, Fan F, Jia Z, Xiaofeng L
Cardiol Young 2022 Jan;32(1):36-41. Epub 2021 Apr 28 doi: 10.1017/S104795112100161X. PMID: 33906700
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Lluri G, Aboulhosn J
Clin Cardiol 2014 Feb;37(2):126-30. Epub 2014 Jan 7 doi: 10.1002/clc.22237. PMID: 24399787Free PMC Article

Recent systematic reviews

Alzghari T, Sandner S, Di Franco A, Harik L, Perezgorvas-Olaria R, Soletti G Jr, Dimagli A, Cancelli G, Demetres M, Lau C, Girardi LN, Gaudino M
Heart Lung Circ 2023 Dec;32(12):1500-1511. Epub 2023 Nov 3 doi: 10.1016/j.hlc.2023.09.014. PMID: 37923692
Guenther TM, Chen SA, Gustafson JD, Ing FF, Brothers JA, Raff GW
Cardiol Young 2021 Oct;31(10):1563-1570. Epub 2021 Jul 26 doi: 10.1017/S1047951121002997. PMID: 34304753
Guenther TM, Sherazee EA, Gustafson JD, Wozniak CJ, Brothers J, Raff G
World J Pediatr Congenit Heart Surg 2020 Nov;11(6):765-775. doi: 10.1177/2150135120938705. PMID: 33164690
Guenther TM, Sherazee EA, Wisneski AD, Gustafson JD, Wozniak CJ, Raff GW
Ann Thorac Surg 2020 Sep;110(3):1063-1071. Epub 2020 Mar 7 doi: 10.1016/j.athoracsur.2020.01.082. PMID: 32156586
Keir M, Bhagra C, Vatenmakher D, Arancibia-Galilea F, Jansen K, Toh N, Silversides CK, Colman J, Siu SC, Sermer M, Crean AM, Wald RM
Cardiol Young 2017 Oct;27(8):1529-1537. Epub 2017 Apr 17 doi: 10.1017/S1047951117000658. PMID: 28412993

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