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Functioning pituitary gland adenoma

MedGen UID:
163135
Concept ID:
C0854486
Neoplastic Process
Synonyms: Endocrine active pituitary adenoma; endocrine active pituitary adenoma; Functioning Adenoma of Pituitary; functioning adenoma of pituitary; Functioning Adenoma of Pituitary Gland; functioning adenoma of pituitary gland; Functioning Adenoma of the Pituitary; functioning adenoma of the pituitary; Functioning Adenoma of the Pituitary Gland; functioning adenoma of the pituitary gland; Functioning PitNET/Adenoma; Functioning Pituitary Adenoma; functioning pituitary adenoma; Functioning pituitary adenoma; Functioning Pituitary Gland Adenoma; functioning pituitary gland adenoma; functioning pituitary gland adenoma (benign); Functioning Pituitary Neuroendocrine Tumor; Functioning Pituitary Neuroendocrine Tumor/Adenoma; Secreting pituitary adenoma; secreting pituitary adenoma; Secretory Adenoma of Pituitary; secretory adenoma of pituitary; Secretory Adenoma of Pituitary Gland; secretory adenoma of pituitary gland; Secretory Adenoma of the Pituitary; secretory adenoma of the pituitary; Secretory Adenoma of the Pituitary Gland; secretory adenoma of the pituitary gland; Secretory Pituitary Adenoma; secretory pituitary adenoma; Secretory Pituitary Gland Adenoma; secretory pituitary gland adenoma
 
Monarch Initiative: MONDO:0003429
Orphanet: ORPHA314753

Definition

A hormone producing pituitary neuroendocrine tumor associated with a hormonal syndrome. [from NCI]

Professional guidelines

PubMed

Tritos NA, Miller KK
JAMA 2023 Apr 25;329(16):1386-1398. doi: 10.1001/jama.2023.5444. PMID: 37097352
Ershadinia N, Tritos NA
Mayo Clin Proc 2022 Feb;97(2):333-346. doi: 10.1016/j.mayocp.2021.11.007. PMID: 35120696
Fleseriu M, Biller BMK, Freda PU, Gadelha MR, Giustina A, Katznelson L, Molitch ME, Samson SL, Strasburger CJ, van der Lely AJ, Melmed S
Pituitary 2021 Feb;24(1):1-13. Epub 2020 Oct 20 doi: 10.1007/s11102-020-01091-7. PMID: 33079318Free PMC Article

Recent clinical studies

Etiology

Villa C, Baussart B, Assié G, Raverot G, Roncaroli F
Endocr Relat Cancer 2023 Aug 1;30(8) Epub 2023 Jun 22 doi: 10.1530/ERC-23-0021. PMID: 37068095
Luger A, Broersen LHA, Biermasz NR, Biller BMK, Buchfelder M, Chanson P, Jorgensen JOL, Kelestimur F, Llahana S, Maiter D, Mintziori G, Petraglia F, Verkauskiene R, Webb SM, Dekkers OM
Eur J Endocrinol 2021 Aug 23;185(3):G1-G33. doi: 10.1530/EJE-21-0462. PMID: 34425558
Drummond J, Roncaroli F, Grossman AB, Korbonits M
J Clin Endocrinol Metab 2019 Jul 1;104(7):2473-2489. doi: 10.1210/jc.2018-00688. PMID: 30020466Free PMC Article
Higham CE, Johannsson G, Shalet SM
Lancet 2016 Nov 12;388(10058):2403-2415. Epub 2016 Mar 31 doi: 10.1016/S0140-6736(16)30053-8. PMID: 27041067
Nieman LK, Biller BM, Findling JW, Murad MH, Newell-Price J, Savage MO, Tabarin A; Endocrine Society
J Clin Endocrinol Metab 2015 Aug;100(8):2807-31. Epub 2015 Jul 29 doi: 10.1210/jc.2015-1818. PMID: 26222757Free PMC Article

Diagnosis

Luger A, Broersen LHA, Biermasz NR, Biller BMK, Buchfelder M, Chanson P, Jorgensen JOL, Kelestimur F, Llahana S, Maiter D, Mintziori G, Petraglia F, Verkauskiene R, Webb SM, Dekkers OM
Eur J Endocrinol 2021 Aug 23;185(3):G1-G33. doi: 10.1530/EJE-21-0462. PMID: 34425558
Reincke M, Honegger J
Exp Clin Endocrinol Diabetes 2021 Mar;129(3):143-145. Epub 2021 Mar 9 doi: 10.1055/a-1369-8898. PMID: 33690869
Drummond J, Roncaroli F, Grossman AB, Korbonits M
J Clin Endocrinol Metab 2019 Jul 1;104(7):2473-2489. doi: 10.1210/jc.2018-00688. PMID: 30020466Free PMC Article
Lake MG, Krook LS, Cruz SV
Am Fam Physician 2013 Sep 1;88(5):319-27. PMID: 24010395
Freda PU, Beckers AM, Katznelson L, Molitch ME, Montori VM, Post KD, Vance ML; Endocrine Society
J Clin Endocrinol Metab 2011 Apr;96(4):894-904. doi: 10.1210/jc.2010-1048. PMID: 21474686Free PMC Article

Therapy

Tritos NA, Miller KK
JAMA 2023 Apr 25;329(16):1386-1398. doi: 10.1001/jama.2023.5444. PMID: 37097352
Wichlińska-Lubińska M, Kozera G
Neurol Neurochir Pol 2019;53(6):413-420. Epub 2019 Nov 20 doi: 10.5603/PJNNS.a2019.0054. PMID: 31745969
Walz PC, Drapeau A, Shaikhouni A, Eide J, Rugino AJ, Mohyeldin A, Carrau R, Prevedello D
Childs Nerv Syst 2019 Nov;35(11):2107-2118. Epub 2019 Jul 13 doi: 10.1007/s00381-019-04293-y. PMID: 31302729
Higham CE, Johannsson G, Shalet SM
Lancet 2016 Nov 12;388(10058):2403-2415. Epub 2016 Mar 31 doi: 10.1016/S0140-6736(16)30053-8. PMID: 27041067
Müller HL
Handb Clin Neurol 2014;124:235-53. doi: 10.1016/B978-0-444-59602-4.00016-2. PMID: 25248591

Prognosis

Villa C, Baussart B, Assié G, Raverot G, Roncaroli F
Endocr Relat Cancer 2023 Aug 1;30(8) Epub 2023 Jun 22 doi: 10.1530/ERC-23-0021. PMID: 37068095
Boguszewski CL, de Castro Musolino NR, Kasuki L
Best Pract Res Clin Endocrinol Metab 2019 Apr;33(2):101268. Epub 2019 Apr 13 doi: 10.1016/j.beem.2019.04.002. PMID: 31027975
Drummond J, Roncaroli F, Grossman AB, Korbonits M
J Clin Endocrinol Metab 2019 Jul 1;104(7):2473-2489. doi: 10.1210/jc.2018-00688. PMID: 30020466Free PMC Article
Ben-Shlomo A, Cooper O
Pituitary 2018 Apr;21(2):183-193. doi: 10.1007/s11102-018-0864-8. PMID: 29344907
Freda PU, Beckers AM, Katznelson L, Molitch ME, Montori VM, Post KD, Vance ML; Endocrine Society
J Clin Endocrinol Metab 2011 Apr;96(4):894-904. doi: 10.1210/jc.2010-1048. PMID: 21474686Free PMC Article

Clinical prediction guides

Villa C, Baussart B, Assié G, Raverot G, Roncaroli F
Endocr Relat Cancer 2023 Aug 1;30(8) Epub 2023 Jun 22 doi: 10.1530/ERC-23-0021. PMID: 37068095
Chanson P, Wolf P
Presse Med 2021 Dec;50(4):104086. Epub 2021 Oct 28 doi: 10.1016/j.lpm.2021.104086. PMID: 34718111
Ilie MD, Jouanneau E, Raverot G
Endocrinol Metab Clin North Am 2020 Sep;49(3):505-515. Epub 2020 Jul 8 doi: 10.1016/j.ecl.2020.05.008. PMID: 32741485
Higham CE, Johannsson G, Shalet SM
Lancet 2016 Nov 12;388(10058):2403-2415. Epub 2016 Mar 31 doi: 10.1016/S0140-6736(16)30053-8. PMID: 27041067
Lake MG, Krook LS, Cruz SV
Am Fam Physician 2013 Sep 1;88(5):319-27. PMID: 24010395

Recent systematic reviews

Rikvold SD, Pedersen MB, Andreassen M, Krogh J
Horm Metab Res 2023 Jul;55(7):443-451. Epub 2023 Jul 10 doi: 10.1055/a-2096-1340. PMID: 37494058
Botelho MS, Franzini ÍA, Nunes-Nogueira VDS, Boguszewski CL
Pituitary 2022 Dec;25(6):810-818. Epub 2022 Jul 28 doi: 10.1007/s11102-022-01257-5. PMID: 35902444
Pertichetti M, Serioli S, Belotti F, Mattavelli D, Schreiber A, Cappelli C, Padovani A, Gasparotti R, Nicolai P, Fontanella MM, Doglietto F
Neurosurg Rev 2020 Aug;43(4):1065-1078. Epub 2019 Jun 27 doi: 10.1007/s10143-019-01134-z. PMID: 31250149
Roca E, Mattogno PP, Porcelli T, Poliani L, Belotti F, Schreiber A, Maffezzoni F, Fontanella MM, Doglietto F
World Neurosurg 2018 Jun;114:e158-e164. Epub 2018 Mar 6 doi: 10.1016/j.wneu.2018.02.120. PMID: 29501516
Kreitschmann-Andermahr I, Siegel S, Weber Carneiro R, Maubach JM, Harbeck B, Brabant G
Clin Endocrinol (Oxf) 2013 Dec;79(6):760-9. Epub 2013 Sep 20 doi: 10.1111/cen.12314. PMID: 23941570

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