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Biphasic synovial sarcoma

MedGen UID:
137773
Concept ID:
C0334507
Neoplastic Process
Synonyms: Biphasic Sarcoma of Synovium; biphasic sarcoma of synovium; Biphasic Sarcoma of the Synovium; biphasic sarcoma of the synovium; Biphasic Synovial Sarcoma; biphasic synovial sarcoma; Synovial sarcoma - biphasic; Synovial sarcoma, biphasic; synovial sarcoma, biphasic; synovial sarcoma, biphasic (morphologic abnormality)
SNOMED CT: Synovial sarcoma - biphasic (18588008); Synovial sarcoma, biphasic (18588008)
 
Monarch Initiative: MONDO:0003468

Definition

A synovial sarcoma characterized by the presence of both an epithelial and a spindle cell component. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBiphasic synovial sarcoma

Professional guidelines

PubMed

Stephens FO, Tattersall MH, Marsden W, Waugh RC, Green D, McCarthy SW
Cancer 1987 Aug 15;60(4):724-35. doi: 10.1002/1097-0142(19870815)60:4<724::aid-cncr2820600404>3.0.co;2-1. PMID: 3474053

Recent clinical studies

Etiology

Graham RP, Nair AA, Davila JI, Jin L, Jen J, Sukov WR, Wu TT, Appelman HD, Torres-Mora J, Perry KD, Zhang L, Kloft-Nelson SM, Knudson RA, Greipp PT, Folpe AL
Mod Pathol 2017 Oct;30(10):1443-1452. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.68. PMID: 28731043
Doyle LA, Wang WL, Dal Cin P, Lopez-Terrada D, Mertens F, Lazar AJ, Fletcher CD, Hornick JL
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ten Heuvel SE, Hoekstra HJ, Bastiaannet E, Suurmeijer AJ
Appl Immunohistochem Mol Morphol 2009 May;17(3):189-95. doi: 10.1097/PAI.0b013e31818a6f5c. PMID: 18997619
Kilpatrick SE, Teot LA, Stanley MW, Ward WG, Savage PD, Geisinger KR
Am J Clin Pathol 1996 Dec;106(6):769-75. doi: 10.1093/ajcp/106.6.769. PMID: 8980353
Aisner SC, Seidman JD, Burke KC, Young JW
Acta Cytol 1993 May-Jun;37(3):413-7. PMID: 7684548

Diagnosis

Liang D, Meng L, Wang S, Yi D, Liu Y
Diagn Pathol 2022 Jun 2;17(1):49. doi: 10.1186/s13000-022-01233-4. PMID: 35655305Free PMC Article
Xia S, Chen X, Hu Y, Zhang J
J Stomatol Oral Maxillofac Surg 2020 Nov;121(5):592-598. Epub 2020 Feb 25 doi: 10.1016/j.jormas.2020.02.005. PMID: 32109597
Wigand MC, Hoffmann TK, Barth TFE, Veit J
Auris Nasus Larynx 2018 Jun;45(3):617-621. Epub 2017 Jul 6 doi: 10.1016/j.anl.2017.06.007. PMID: 28689931
Hisaoka M, Matsuyama A, Shimajiri S, Akiba J, Kusano H, Hiraoka K, Shoda T, Hashimoto H
Pathol Res Pract 2009;205(3):195-8. Epub 2008 Nov 28 doi: 10.1016/j.prp.2008.10.003. PMID: 19041192
Fisher C
Ann Diagn Pathol 1998 Dec;2(6):401-21. doi: 10.1016/s1092-9134(98)80042-7. PMID: 9930576

Therapy

Bae YJ, Kim H, Cha W, Choi BS
Medicine (Baltimore) 2021 Dec 30;100(52):e28411. doi: 10.1097/MD.0000000000028411. PMID: 34967377Free PMC Article
Vakili R, Hiradfar M, Zabolinejad N, Badiei Z
J Pediatr Endocrinol Metab 2007 Jul;20(7):841-5. doi: 10.1515/jpem.2007.20.7.841. PMID: 17849748
Bilgic B, Mete O, Oztürk SA, Demiryont M, Keles N, Basaran M
Pathol Oncol Res 2003;9(4):242-5. Epub 2003 Dec 22 doi: 10.1007/BF02893385. PMID: 14688831
Kasai T, Shimajiri S, Hashimoto H
Mol Pathol 2000 Apr;53(2):107-10. doi: 10.1136/mp.53.2.107. PMID: 10889911Free PMC Article
Stephens FO, Tattersall MH, Marsden W, Waugh RC, Green D, McCarthy SW
Cancer 1987 Aug 15;60(4):724-35. doi: 10.1002/1097-0142(19870815)60:4<724::aid-cncr2820600404>3.0.co;2-1. PMID: 3474053

Prognosis

Xia S, Chen X, Hu Y, Zhang J
J Stomatol Oral Maxillofac Surg 2020 Nov;121(5):592-598. Epub 2020 Feb 25 doi: 10.1016/j.jormas.2020.02.005. PMID: 32109597
Nicola M, Onorati M, Bertola G, Collini P, Fascì AI, Di Nuovo F
Pathologica 2018 Sep;110(2):106-110. PMID: 30546147
Graham RP, Nair AA, Davila JI, Jin L, Jen J, Sukov WR, Wu TT, Appelman HD, Torres-Mora J, Perry KD, Zhang L, Kloft-Nelson SM, Knudson RA, Greipp PT, Folpe AL
Mod Pathol 2017 Oct;30(10):1443-1452. Epub 2017 Jul 21 doi: 10.1038/modpathol.2017.68. PMID: 28731043
Alcaraz-García P, Díaz-Palacios S, Castillo-Canto C, Gatica-Pérez A, Sánchez-González JA
Cir Cir 2012 Jan-Feb;80(1):67-71. PMID: 22472156
Fisher C
Ann Diagn Pathol 1998 Dec;2(6):401-21. doi: 10.1016/s1092-9134(98)80042-7. PMID: 9930576

Clinical prediction guides

Xia S, Chen X, Hu Y, Zhang J
J Stomatol Oral Maxillofac Surg 2020 Nov;121(5):592-598. Epub 2020 Feb 25 doi: 10.1016/j.jormas.2020.02.005. PMID: 32109597
Lenz J, Chvátal R, Fiala L, Kavka M
Ceska Gynekol 2019 Spring;84(3):212-215. PMID: 31324112
Nicola M, Onorati M, Bertola G, Collini P, Fascì AI, Di Nuovo F
Pathologica 2018 Sep;110(2):106-110. PMID: 30546147
Schaefer IM, Agaimy A, Fletcher CD, Hornick JL
Mod Pathol 2017 Apr;30(4):539-548. Epub 2017 Jan 13 doi: 10.1038/modpathol.2016.230. PMID: 28084340
Alcaraz-García P, Díaz-Palacios S, Castillo-Canto C, Gatica-Pérez A, Sánchez-González JA
Cir Cir 2012 Jan-Feb;80(1):67-71. PMID: 22472156

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