Neoplasm of the peripheral nervous system

MedGen UID:: 45817
•Concept ID:: C0031118
•: Neoplastic Process

Synonyms:	Neoplasm, Peripheral Nerve; Neoplasms, Peripheral Nerve; Nerve Neoplasm, Peripheral; Nerve Neoplasms, Peripheral; Nerve Tumor, Peripheral; Nerve Tumors, Peripheral; Peripheral Nerve Neoplasm; Peripheral Nerve Neoplasms; Peripheral Nerve Tumor; Peripheral Nerve Tumors; Peripheral Nervous System Neoplasms; Tumor, Peripheral Nerve; Tumors, Peripheral Nerve
SNOMED CT:	Neoplasm of peripheral nerve (126980002); Tumor of peripheral nerve (126980002)

HPO:	HP:0100007
Monarch Initiative:	MONDO:0001406

Definition

A benign or malignant neoplasm (tumor) of the peripheral nervous system. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVNeoplasm of the peripheral nervous system

Abnormality of prenatal development or birth
- Fetal anomaly
  - Congenital Systemic Disorder
    - Abnormality of the nervous system
      - Abnormal nervous system morphology
        Neoplasm of the nervous system
        Neoplasm of the peripheral nervous system
        Autonomic nervous system neoplasm
        Ganglioneuroma
        Colorectal Ganglioneuroma
        Hypothalamic Gangliocytoma
        Mature Ganglioneuroma
        Maturing Ganglioneuroma
        Mediastinal Ganglioneuroma
        Presacral ganglioneuroma
        Recurrent Gangliocytoma
        Retroperitoneal Ganglioneuroma
        Cutaneous Neural Neoplasm
        Benign dermal neurilemmoma
        Cutaneous ganglioneuroma
        Cutaneous granular cell tumor
        Cutaneous Neurofibroma
        Cutaneous Perineurioma
        Dermal Nerve Sheath Myxoma
        Malignant Peripheral Nerve Sheath Tumor of the Skin
        Epithelioid Malignant Peripheral Nerve Sheath Tumor of the Skin
        Lipomatosis of Nerve
        Neurofibromatosis
        Aggravated Neurofibromatosis
        Neurofibroma by anatomical location
        Cardiac neurofibroma
        Gastric neurofibroma
        Paraspinal neurofibroma
        Renal neurofibroma
        Spinal neurofibroma
        Subcutaneous neurofibroma
        Tongue neurofibroma
        Neurofibromatosis, type IV, of Riccardi
        Plexiform neurofibroma
        Unresectable Plexiform Neurofibroma
        Neuroma
        Appendix Neuroma
        Multiple mucosal neuromas
        Traumatic neuroma
        Morton neuroma
        Neuroma of amputation stump
        Peripheral neuroepithelioma
        Askin tumor
        Localized Askin Tumor
        Recurrent Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor
        Ewing sarcoma
        Atypical Ewing Sarcoma
        Localized Ewing Sarcoma
        Metastatic Ewing Sarcoma
        Recurrent Ewing Sarcoma
        Refractory Ewing Sarcoma
        Unresectable Ewing Sarcoma
        Schwannoma
        Acoustic neuroma
        Bilateral vestibular schwannoma
        Unilateral vestibular schwannoma
        Ancient Schwannoma
        Conventional Schwannoma
        Epithelioid Schwannoma
        Peripheral schwannoma
        Sellar Schwannoma
        Sinonasal Schwannoma

Professional guidelines

PubMed

EANO guideline on the diagnosis and treatment of vestibular schwannoma.

Goldbrunner R, Weller M, Regis J, Lund-Johansen M, Stavrinou P, Reuss D, Evans DG, Lefranc F, Sallabanda K, Falini A, Axon P, Sterkers O, Fariselli L, Wick W, Tonn JC
Neuro Oncol 2020 Jan 11;22(1):31-45. doi: 10.1093/neuonc/noz153. PMID: 31504802 Free PMC Article

Updates in Diagnosis, Management, and Treatment of Neuroblastoma.

Swift CC, Eklund MJ, Kraveka JM, Alazraki AL
Radiographics 2018 Mar-Apr;38(2):566-580. doi: 10.1148/rg.2018170132. PMID: 29528815

Clinical practice guidelines on the evidence-based use of integrative therapies during and after breast cancer treatment.

Greenlee H, DuPont-Reyes MJ, Balneaves LG, Carlson LE, Cohen MR, Deng G, Johnson JA, Mumber M, Seely D, Zick SM, Boyce LM, Tripathy D
CA Cancer J Clin 2017 May 6;67(3):194-232. Epub 2017 Apr 24 doi: 10.3322/caac.21397. PMID: 28436999 Free PMC Article

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Recent clinical studies

Diagnosis

The pivotal role of sampling recurrent tumors in the precision care of patients with tumors of the central nervous system.

Wong D, Shen Y, Levine AB, Pleasance E, Jones M, Mungall K, Thiessen B, Toyota B, Laskin J, Jones SJM, Marra MA, Yip S
Cold Spring Harb Mol Case Stud 2019 Aug;5(4) Epub 2019 Aug 1 doi: 10.1101/mcs.a004143. PMID: 31371350 Free PMC Article

Primitive neuroectodermal tumor of the pancreas. An extremely rare tumor. Case report and review of the literature.

Bülchmann G, Schuster T, Haas RJ, Joppich I
Klin Padiatr 2000 Jul-Aug;212(4):185-8. doi: 10.1055/s-2000-9675. PMID: 10994548

See all (2)